《英文msh词典》Anemia,Diamond Blackfan
[入口词] Anemia,Diamond Blackfan
[主题词] Anemia,Diamond-Blackfan
[英文释义] A rare congenital hypoplastic anemia that usually presents early in infancy. The disease is characterized by a moderate to severe macrocytic anemia,occasional neutropenia or thrombocytosis,a normocellular bone marrow with erythroid hypoplasia,and an increased risk of developing leukemia. (Curr Opin Hematol 2000 Mar;7(2):85-94)