《英文msh词典》Acid,Methylmalonic
[入口词] Acid,Methylmalonic
[主题词] Methylmalonic Acid
[英文释义] A malonic acid derivative which is a vital intermediate in the metabolism of fat and protein. Abnormalities in methylmalonic acid metabolism lead to methylmalonic aciduria. This metabolic disease is attributed to a block in the enzymatic conversion of methylmalonyl CoA to succinyl CoA.