《英文msh词典》Aganglionosis,Colonic
[同义词] Aganglionosis,Colonic
[主题词] Hirschsprung Disease
[中文释义] 神经节细胞缺乏症,结肠
[英文释义] Congenital MEGACOLON resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the LARGE INTESTINE. The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases,the aganglionic segment is within the RECTUM and SIGMOID COLON.